Table 3. Main characteristics of... | American Society of Hematology

Table 3.

Main characteristics of patients with FHL

	Patients with FHL2, UPN									Patients with FHL3, UPN
Characteristic	210	235	256	314	306	180	225	237	249	277	289	293	336
Age at diagnosis, mo	2	3	60	2	4	2	144	84	96	108	3	2	4
Sex	M	F	M	F	F	F	F	M	F	M	M	F	M
Fever	+	+	+	+	+	+	+	+	+	+	+	-	+
Splenomegaly	+	+	+	+	+	+	+	+	+	+	+	+	+
Cytopenia	+	+	+	+	+	+	+	+	+	+	+	+	+
Hypertriglyceridemia	ND	+	+	+	+	+	+	ND	-	+	-	+	+
Hypofibrinogenemia	+	-	+	+	+	+	-	+	-	+	+	+	+
HSCT	Y	Y	N	Y	Y	N	N	Y	Y	Y	N	Y	Y
Outcome	DoD	Alive	Alive	DoD	Alive	DoD	DoT	Alive	Alive	Alive	DoD	Alive	Alive

	Patients with FHL2, UPN									Patients with FHL3, UPN
Characteristic	210	235	256	314	306	180	225	237	249	277	289	293	336
Age at diagnosis, mo	2	3	60	2	4	2	144	84	96	108	3	2	4
Sex	M	F	M	F	F	F	F	M	F	M	M	F	M
Fever	+	+	+	+	+	+	+	+	+	+	+	-	+
Splenomegaly	+	+	+	+	+	+	+	+	+	+	+	+	+
Cytopenia	+	+	+	+	+	+	+	+	+	+	+	+	+
Hypertriglyceridemia	ND	+	+	+	+	+	+	ND	-	+	-	+	+
Hypofibrinogenemia	+	-	+	+	+	+	-	+	-	+	+	+	+
HSCT	Y	Y	N	Y	Y	N	N	Y	Y	Y	N	Y	Y
Outcome	DoD	Alive	Alive	DoD	Alive	DoD	DoT	Alive	Alive	Alive	DoD	Alive	Alive

UPN indicates unique patient number; HSCT, allogeneic hematopoietic stem cell transplantation; +, present; -, absent; ND, not determined; DoD, dead of disease; and DoT, dead of toxicity.