Table 5. Survival as reported in the 3... | American Society of Hematology

Table 5.

Survival as reported in the 3 largest reports on HLH

Publication	Year of report	Number of patients	Survival
Janka (review)¹	1983	121	5% (1 yr)^5-150
Arico et al²	1996	122	22% (5 yr)^5-151
Present study	2002	113	55% (5 yr)^5-151
Present study (familial cases)	2002	25	51% (5 yr)^5-151

Publication	Year of report	Number of patients	Survival
Janka (review)¹	1983	121	5% (1 yr)^5-150
Arico et al²	1996	122	22% (5 yr)^5-151
Present study	2002	113	55% (5 yr)^5-151
Present study (familial cases)	2002	25	51% (5 yr)^5-151

Of 121 patients reviewed, 5 of 101 with follow-up data survived more than 12 months.

Probability of survival according to Kaplan-Meier estimate.