Patient baseline characteristics and reference values
| . | HKD1 . | HKD2 . | PKD1 . | PKD2 . | PKD3 . | Reference values . |
|---|---|---|---|---|---|---|
| Clinical characteristics | ||||||
| Sex (F/M) | F | M | F | M | M | NA |
| Age, y | 61 | 50 | 54 | 63 | 52 | NA |
| Splenectomized (yes/no) | Yes | No | Yes | No | Yes | NA |
| RBC units past 3 months | 8 | 0 | 4 | 0 | 0 | NA |
| Hematological variables | ||||||
| Hb, g/dL | 9.6 | 13.3 | 8.6 | 12.0 | 7.3 | 13.9-17.2 (M); 11.9-15.5 (F) |
| RBC count, × 1012/L | 3.2 | 4.6 | 2.9 | 3.6 | 2.0 | 4.2-5.5 (M); 3.7-5.0 (F) |
| HCT, L/L | 0.30 | 0.43 | 0.28 | 0.33 | 0.25 | 0.41-0.5 (M); 0.36-0.46 (F) |
| MCV, fL | 95 | 93 | 97 | 90 | 125 | 80-97 |
| MCHC, g/dL | 32.1 | 31.1 | 30.9 | 36.7 | 29.5 | 30.637.1 |
| ARC, × 109/L | 395 | 64 | 875 | 286 | 1271 | 25-120 |
| Enzyme activities | ||||||
| PK activity, U/g Hb | 8.5 | 6.5 | 6.2 | 1.7 | 1.0 | 6.6-15.4 |
| HK activity, U/g Hb | 0.7 | 0.8 | 4.1 | 1.6 | 6.5 | 0.9-1.7 |
| PK/HK ratio | 12.1 | 8.1 | 1.5 | 1.1 | 0.2 | 6.6-11.8 |
| . | HKD1 . | HKD2 . | PKD1 . | PKD2 . | PKD3 . | Reference values . |
|---|---|---|---|---|---|---|
| Clinical characteristics | ||||||
| Sex (F/M) | F | M | F | M | M | NA |
| Age, y | 61 | 50 | 54 | 63 | 52 | NA |
| Splenectomized (yes/no) | Yes | No | Yes | No | Yes | NA |
| RBC units past 3 months | 8 | 0 | 4 | 0 | 0 | NA |
| Hematological variables | ||||||
| Hb, g/dL | 9.6 | 13.3 | 8.6 | 12.0 | 7.3 | 13.9-17.2 (M); 11.9-15.5 (F) |
| RBC count, × 1012/L | 3.2 | 4.6 | 2.9 | 3.6 | 2.0 | 4.2-5.5 (M); 3.7-5.0 (F) |
| HCT, L/L | 0.30 | 0.43 | 0.28 | 0.33 | 0.25 | 0.41-0.5 (M); 0.36-0.46 (F) |
| MCV, fL | 95 | 93 | 97 | 90 | 125 | 80-97 |
| MCHC, g/dL | 32.1 | 31.1 | 30.9 | 36.7 | 29.5 | 30.637.1 |
| ARC, × 109/L | 395 | 64 | 875 | 286 | 1271 | 25-120 |
| Enzyme activities | ||||||
| PK activity, U/g Hb | 8.5 | 6.5 | 6.2 | 1.7 | 1.0 | 6.6-15.4 |
| HK activity, U/g Hb | 0.7 | 0.8 | 4.1 | 1.6 | 6.5 | 0.9-1.7 |
| PK/HK ratio | 12.1 | 8.1 | 1.5 | 1.1 | 0.2 | 6.6-11.8 |
ARC, absolute reticulocyte count; F, female; Hb, hemoglobin; HCT, hematocrit; M, male; MCHC, mean corpuscular hemoglobin concentration; MCV, mean corpuscular volume; NA, not applicable.