Scores of FVIII RR to DDAVP
| RR . | |||||
|---|---|---|---|---|---|
| . | Total . | Absent . | Partial . | Complete . | P value . |
| F8 variants, n (%) | |||||
| Null | 143 | 21 (14.7) | 65 (45.5) | 55 (38.5) | .0454 |
| Non-null | 218 | 16 (7.3) | 98 (45.0) | 104 (47.7) | |
| Severity of the familial HA, n (%) | |||||
| Severe/moderate | 216 | 27 (12.5) | 107 (49.5) | 82 (38.0) | .0170 |
| Mild | 145 | 10 (6.9) | 59 (40.7) | 76 (52.4) | |
| Basal VWF levels (IU/mL), n (%) | |||||
| <0.7 | 127 | 6 (4.7) | 49 (38.6) | 72 (56.7) | .0001 |
| ≥0.7 | 207 | 29 (14.0) | 106 (51.2) | 72 (34.8) | |
| Blood group, n (%) | |||||
| O | 195 | 20 (10.3) | 88 (45.1) | 87 (44.6) | .4704 |
| Non-O | 118 | 10 (8.5) | 62 (52.5) | 46 (39.0) | |
| Age (y), n (%) | |||||
| ≤18 | 125 | 17 (13.6) | 64 (51.2) | 44 (35.2) | .0331 |
| >18 | 236 | 20 (8.5) | 101 (42.8) | 115 (48.7) | |
| Body weight (kg), n (%) | |||||
| ≤35 | 72 | 13 (18.1) | 40 (55.6) | 19 (26.4) | .0130 |
| 35-70 | 271 | 22 (8.1) | 114 (42.1) | 121 (44.6) | |
| >70 | 18 | 1 (5.6) | 8 (44.4) | 9 (50.0) | |
| DDAVP doses (μg/kg), n (%) | |||||
| ≤0.3 | 263 | 31 (11.8) | 125 (47.5) | 107 (40.7) | .0498 |
| >0.3 | 83 | 5 (6.0) | 32 (38.6) | 46 (55.4) | |
| RR . | |||||
|---|---|---|---|---|---|
| . | Total . | Absent . | Partial . | Complete . | P value . |
| F8 variants, n (%) | |||||
| Null | 143 | 21 (14.7) | 65 (45.5) | 55 (38.5) | .0454 |
| Non-null | 218 | 16 (7.3) | 98 (45.0) | 104 (47.7) | |
| Severity of the familial HA, n (%) | |||||
| Severe/moderate | 216 | 27 (12.5) | 107 (49.5) | 82 (38.0) | .0170 |
| Mild | 145 | 10 (6.9) | 59 (40.7) | 76 (52.4) | |
| Basal VWF levels (IU/mL), n (%) | |||||
| <0.7 | 127 | 6 (4.7) | 49 (38.6) | 72 (56.7) | .0001 |
| ≥0.7 | 207 | 29 (14.0) | 106 (51.2) | 72 (34.8) | |
| Blood group, n (%) | |||||
| O | 195 | 20 (10.3) | 88 (45.1) | 87 (44.6) | .4704 |
| Non-O | 118 | 10 (8.5) | 62 (52.5) | 46 (39.0) | |
| Age (y), n (%) | |||||
| ≤18 | 125 | 17 (13.6) | 64 (51.2) | 44 (35.2) | .0331 |
| >18 | 236 | 20 (8.5) | 101 (42.8) | 115 (48.7) | |
| Body weight (kg), n (%) | |||||
| ≤35 | 72 | 13 (18.1) | 40 (55.6) | 19 (26.4) | .0130 |
| 35-70 | 271 | 22 (8.1) | 114 (42.1) | 121 (44.6) | |
| >70 | 18 | 1 (5.6) | 8 (44.4) | 9 (50.0) | |
| DDAVP doses (μg/kg), n (%) | |||||
| ≤0.3 | 263 | 31 (11.8) | 125 (47.5) | 107 (40.7) | .0498 |
| >0.3 | 83 | 5 (6.0) | 32 (38.6) | 46 (55.4) | |