Table 1.

Simplistic overview of classification schema of vascular anomalies

Vascular tumorsVascular malformations
HemangiomaSlow flowFast flowOther/unclassified
 Infantile
 Congenital
  Rapidly involutinga
  Noninvoluting
KHEa
TAa 
CM
VMa
LM
 Macro- or microcystic LM
 GLA
 KLAa
Combined malformation
 CVMa
 CLMa
 CLVMa
 VLMa
 PROSa
 KTSa
 CLOVESa 
Arteriovenous
Arteriovenous fistula 
Malformation MLTa 
Vascular tumorsVascular malformations
HemangiomaSlow flowFast flowOther/unclassified
 Infantile
 Congenital
  Rapidly involutinga
  Noninvoluting
KHEa
TAa 
CM
VMa
LM
 Macro- or microcystic LM
 GLA
 KLAa
Combined malformation
 CVMa
 CLMa
 CLVMa
 VLMa
 PROSa
 KTSa
 CLOVESa 
Arteriovenous
Arteriovenous fistula 
Malformation MLTa 
a

These conditions can be associated with various types of coagulation derangements.

CLM, capillary-lymphatic malformation; CLOVES, congenital lipomatous (fatty) overgrowth, vascular malformations, epidermal nevi, and scoliosis/ skeletal/spinal anomalies; CLVM, capillary-lymphatic-venous malformation; CM, capillary malformation; CVM, capillary-venous malformation; GLA, generalized lymphatic anomaly; KHE, kaposiform hemangioendothelioma; KLA, kaposiform lymphangiomatosis; KTS, Klippel-Trenaunay syndrome; LM, lymphatic malformation; MLT, multifocal lymphangiomatosis with thrombocytopenia; PROS, PIK3CA-related overgrowth syndrome; TA, tufted angioma; VLM, venous-lymphatic malformation; VM, venous malformation.

Adapted and reprinted from Crary and Mack2 with permission.

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