Table 1.

PegIFN in MPN: who and why

MPN subtypeTarget populationWhyFDA/EMA approval
Polycythemia vera
 
High-risk first line • High rate of CHR
• High rate of MR
• Possible EFS improvement 
Yes/yes
Only for ropegINF-α2b 
High-risk second line • High rate of CHR
• High rate of MR
• Possible EFS improvement 
Yes/yes
Only for ropegINF-α2b 
Low risk In only 1 study, compared to PHL + ASA:
• Higher rate of CHR
• Improvement in symptoms
• Higher rate of MR 
Yes/yes
Only for ropegINF-α2b 
Pregnancy • Reduced risk of miscarriage
• Improved maternal and fetal outcomes 
No/no 
Essential thrombocythemia
 
High-risk first line • High rate of CHR
• High rate of MR 
No/no 
High-risk second line • High rate of CHR
• High rate of MR 
No/no
Ongoing phase 3 studies with ropegINF-α2b 
Pregnancy • Reduced risk of miscarriage
• Improved maternal and fetal outcomes 
No/no 
Myelofibrosis
 
Low risk and early stage (splenomegaly <6 cm BCM, no grade 3 fibrosis) • Possible resolution of fibrosis
• Possible MR 
No/no
Ongoing phase 2 studies with ropegINF-α2b 
Prefibrotic myelofibrosis • Possibly avoid disease progression to overt myelofibrosis No/no
Ongoing phase 2 studies with ropegINF-α2b 
MPN subtypeTarget populationWhyFDA/EMA approval
Polycythemia vera
 
High-risk first line • High rate of CHR
• High rate of MR
• Possible EFS improvement 
Yes/yes
Only for ropegINF-α2b 
High-risk second line • High rate of CHR
• High rate of MR
• Possible EFS improvement 
Yes/yes
Only for ropegINF-α2b 
Low risk In only 1 study, compared to PHL + ASA:
• Higher rate of CHR
• Improvement in symptoms
• Higher rate of MR 
Yes/yes
Only for ropegINF-α2b 
Pregnancy • Reduced risk of miscarriage
• Improved maternal and fetal outcomes 
No/no 
Essential thrombocythemia
 
High-risk first line • High rate of CHR
• High rate of MR 
No/no 
High-risk second line • High rate of CHR
• High rate of MR 
No/no
Ongoing phase 3 studies with ropegINF-α2b 
Pregnancy • Reduced risk of miscarriage
• Improved maternal and fetal outcomes 
No/no 
Myelofibrosis
 
Low risk and early stage (splenomegaly <6 cm BCM, no grade 3 fibrosis) • Possible resolution of fibrosis
• Possible MR 
No/no
Ongoing phase 2 studies with ropegINF-α2b 
Prefibrotic myelofibrosis • Possibly avoid disease progression to overt myelofibrosis No/no
Ongoing phase 2 studies with ropegINF-α2b 

ASA, aspirin; BCM, below costal margin, EFS, event-free survival; EMA, European Medicine Agency; FDA, Food and Drug Administration; PHL, phlebotomy.

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