Table 1.

Summary of pregnancy outcomes in MPN patients within last 5 years

StudyNo. of patients/ no. of pregnancies)MPN type (%)Treatments (%)Maternal/Fetal Complications (%)Live births (%)
Elli et al. (2019)39  7/11 PV (100) ASA (91)
IFN (18.2)
LMWH (36) 
Early pregnancy loss (9.1)
Preterm (9.1)
Stillbirth (18.2) 
81.8 
Gangat et al. (2020)25  61/102 ET (90.1)
PV (6.6)
MF (3.3) 
ASA (60)
LMWH (9)
IFN (15) 
Hemorrhage (7)
Thrombosis (4)
Preeclampsia (4)
Early pregnancy loss (31)
Stillbirth (1)
Preterm (2)
IUGR (3) 
67 
Gangat et al. (2021)16  16/24 MF (100) ASA (58.3)
LMWH (30)
pIFN (8.3) 
Hemorrhage (12.5)
Thrombosis (0)
Early pregnancy loss (20.8)
Stillbirth (8.3)
Preterm (8.3)
IUGR (4.2) 
70.8 
How et al. (2020)23  52/121 ET (100) ASA (61.2)
IFN (1.6)
LMWH (31.7) 
Hemorrhage (5.8)
Thrombosis (2.5)
Preeclampsia (3.3)
Gestational HTN (0.8)
Early pregnancy loss (32.2)
Stillbirth (0.8)
Preterm (7.4)
IUGR (2.5) 
69 
İskender et al. (2021)30  21/21 ET (100) ASA (85.7)
LMWH (66.7)
pIFN (9.5) 
Thrombosis (9.5)
Preeclampsia (7.1)
Early pregnancy loss (33.3)
Stillbirth (0)
Preterm (21.4)
IUGR (14.3) 
66.7 
Landtblom et al. (2022)18  229/342 ET (70)
PV (11.8)
MF (10.5)
MPNU (8.7) 
NA Hemorrhage (14)
Thrombosis (1)
Preeclampsia, HELLP, gestational HTN (6)
Preterm (12)
Stillbirth (0.6) 
NA 
Lapoirie et al. (2020)40  14/27 ET (64.3)
PV (35.7) 
ASA (67)
LMWH (66.7)
IFN (22) 
Hemorrhage (11)
Thrombosis (15)
Early pregnancy loss (22.2)
Stillbirth (4)
Preterm (15)
IUGR (15) 
70 
Maze et al. (2023)41  24/29 ET (48)
PV (31)
MF (14)
MPN NOS (7) 
ASA (83)
LMWH (17)
IFN (17)
Anagrelide (10) 
Hemorrhage (3)
Thrombosis (3)
Preeclampsia (0)
Early pregnancy loss (13.8)
Stillbirth (4.2) 
83 
Schrickel et al. (2021)31  23/34 ET (100) ASA (58.8)
LMWH (61.8)
pIFN (58.8)
IFN (41.2) 
Hemorrhage (7.7)
Thrombosis (0)
Preeclampsia (4.2)
Early pregnancy loss (26.5) 
73.5 
Wille et al. (2021)32  20/41 PV (100) ASA (56.1)
LMWH (51.2)
pIFN (7.3)
IFN (7.3) 
Hemorrhage (2.4)
Thrombosis (2.4)
Preeclampsia (2.4)
Early pregnancy loss (44)
Stillbirth (4.9)
Preterm (7.3) 
51.2 
Wille et al. (2023)15  69/129 PV (100) ASA (48)
LMWH (40)
IFN (10.9) 
Hemorrhage (15.5)
Thrombosis (3.1)
Preeclampsia (3.9)
Early pregnancy loss (24.8)
Stillbirth (7)
Preterm (17.8) 
68.2 
StudyNo. of patients/ no. of pregnancies)MPN type (%)Treatments (%)Maternal/Fetal Complications (%)Live births (%)
Elli et al. (2019)39  7/11 PV (100) ASA (91)
IFN (18.2)
LMWH (36) 
Early pregnancy loss (9.1)
Preterm (9.1)
Stillbirth (18.2) 
81.8 
Gangat et al. (2020)25  61/102 ET (90.1)
PV (6.6)
MF (3.3) 
ASA (60)
LMWH (9)
IFN (15) 
Hemorrhage (7)
Thrombosis (4)
Preeclampsia (4)
Early pregnancy loss (31)
Stillbirth (1)
Preterm (2)
IUGR (3) 
67 
Gangat et al. (2021)16  16/24 MF (100) ASA (58.3)
LMWH (30)
pIFN (8.3) 
Hemorrhage (12.5)
Thrombosis (0)
Early pregnancy loss (20.8)
Stillbirth (8.3)
Preterm (8.3)
IUGR (4.2) 
70.8 
How et al. (2020)23  52/121 ET (100) ASA (61.2)
IFN (1.6)
LMWH (31.7) 
Hemorrhage (5.8)
Thrombosis (2.5)
Preeclampsia (3.3)
Gestational HTN (0.8)
Early pregnancy loss (32.2)
Stillbirth (0.8)
Preterm (7.4)
IUGR (2.5) 
69 
İskender et al. (2021)30  21/21 ET (100) ASA (85.7)
LMWH (66.7)
pIFN (9.5) 
Thrombosis (9.5)
Preeclampsia (7.1)
Early pregnancy loss (33.3)
Stillbirth (0)
Preterm (21.4)
IUGR (14.3) 
66.7 
Landtblom et al. (2022)18  229/342 ET (70)
PV (11.8)
MF (10.5)
MPNU (8.7) 
NA Hemorrhage (14)
Thrombosis (1)
Preeclampsia, HELLP, gestational HTN (6)
Preterm (12)
Stillbirth (0.6) 
NA 
Lapoirie et al. (2020)40  14/27 ET (64.3)
PV (35.7) 
ASA (67)
LMWH (66.7)
IFN (22) 
Hemorrhage (11)
Thrombosis (15)
Early pregnancy loss (22.2)
Stillbirth (4)
Preterm (15)
IUGR (15) 
70 
Maze et al. (2023)41  24/29 ET (48)
PV (31)
MF (14)
MPN NOS (7) 
ASA (83)
LMWH (17)
IFN (17)
Anagrelide (10) 
Hemorrhage (3)
Thrombosis (3)
Preeclampsia (0)
Early pregnancy loss (13.8)
Stillbirth (4.2) 
83 
Schrickel et al. (2021)31  23/34 ET (100) ASA (58.8)
LMWH (61.8)
pIFN (58.8)
IFN (41.2) 
Hemorrhage (7.7)
Thrombosis (0)
Preeclampsia (4.2)
Early pregnancy loss (26.5) 
73.5 
Wille et al. (2021)32  20/41 PV (100) ASA (56.1)
LMWH (51.2)
pIFN (7.3)
IFN (7.3) 
Hemorrhage (2.4)
Thrombosis (2.4)
Preeclampsia (2.4)
Early pregnancy loss (44)
Stillbirth (4.9)
Preterm (7.3) 
51.2 
Wille et al. (2023)15  69/129 PV (100) ASA (48)
LMWH (40)
IFN (10.9) 
Hemorrhage (15.5)
Thrombosis (3.1)
Preeclampsia (3.9)
Early pregnancy loss (24.8)
Stillbirth (7)
Preterm (17.8) 
68.2 

The meta-analysis by Maze et al. provides a comprehensive synthesis of 22 studies from 1996-2018.13 

*

Meta-analysis of 22 studies.

ASA, aspirin; HELLP, hemolysis, elevated liver enzymes, and low platelets; HTN, hypertension; IFN, interferon; IUGR, intrauterine growth restriction; MPNU, myeloproliferative neoplasm unclassified; NOS, not otherwise specified; pIFN, pegylated interferon.

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